Amino acid metabolism (WP662)
Mus musculus
A complete overview of the metabolism of all 20 amino acids
Authors
Martijn Van Iersel , Martina Summer-Kutmon , Egon Willighagen , and Eric WeitzActivity
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Organisms
Mus musculusCommunities
Annotations
Pathway Ontology
amino acid metabolic pathway| Label | Type | Compact Identifier | Comment |
|---|---|---|---|
| Ethanol | Metabolite | hmdb:HMDB0000108 | |
| Methionine | Metabolite | hmdb:HMDB0000696 | |
| Indoleacetate | Metabolite | hmdb:HMDB0000197 | |
| Aconitate | Metabolite | hmdb:HMDB0000072 | |
| Oxaloacetate | Metabolite | hmdb:HMDB0000223 | |
| Aspartate | Metabolite | hmdb:HMDB0000191 | |
| Leucine | Metabolite | hmdb:HMDB0000687 | |
| Urea | Metabolite | hmdb:HMDB0000294 | |
| Fumarate | Metabolite | hmdb:HMDB0000134 | |
| isocitrate | Metabolite | hmdb:HMDB0000193 | |
| Citrate | Metabolite | hmdb:HMDB0000094 | |
| methylhistamine | Metabolite | hmdb:HMDB0000898 | |
| Dopamine | Metabolite | hmdb:HMDB0000073 | |
| Cystathionine | Metabolite | hmdb:HMDB0000099 | |
| Carbamoyl-aspartate | Metabolite | hmdb:HMDB0000828 | |
| Histidine | Metabolite | hmdb:HMDB0000177 | |
| Pyruvate | Metabolite | hmdb:HMDB0000243 | |
| 5-OH-Trp | Metabolite | hmdb:HMDB0000472 | |
| B-OH-butyrate | Metabolite | hmdb:HMDB0000011 | |
| Glutamine | Metabolite | hmdb:HMDB0000641 | |
| Glucose | Metabolite | hmdb:HMDB0000122 | |
| Creatine P | Metabolite | hmdb:HMDB0001511 | |
| Threonine | Metabolite | hmdb:HMDB0000167 | |
| Glutamine | Metabolite | hmdb:HMDB0000641 | |
| Glycine | Metabolite | hmdb:HMDB0000123 | |
| Isoleucine | Metabolite | hmdb:HMDB0000172 | |
| Arginine | Metabolite | hmdb:HMDB0000517 | |
| Histamine | Metabolite | hmdb:HMDB0000870 | |
| Melanin | Metabolite | hmdb:HMDB0004068 | |
| Tyrosine | Metabolite | hmdb:HMDB0000158 | |
| Ornithine | Metabolite | hmdb:HMDB0000214 | |
| hydroxy-proline | Metabolite | hmdb:HMDB0000725 | |
| mercaptopyruvate | Metabolite | hmdb:HMDB0001368 | |
| Alanine | Metabolite | hmdb:HMDB0000161 | |
| Asparagine | Metabolite | hmdb:HMDB0000168 | |
| Homocysteine | Metabolite | hmdb:HMDB0000742 | |
| Oxaloacetate | Metabolite | hmdb:HMDB0000223 | |
| Tryptamine | Metabolite | hmdb:HMDB0000303 | |
| carbamoyl-P | Metabolite | hmdb:HMDB0001096 | |
| Succinyl-CoA | Metabolite | hmdb:HMDB0001022 | |
| Citrulline | Metabolite | hmdb:HMDB0000904 | |
| Cysteine | Metabolite | hmdb:HMDB0000574 | |
| Thyroxine | Metabolite | hmdb:HMDB0000248 | |
| Spermidine | Metabolite | hmdb:HMDB0001257 | |
| Glycine | Metabolite | hmdb:HMDB0000123 | |
| oxo-isocaproate | Metabolite | chebi:17865 | |
| Serine | Metabolite | hmdb:HMDB0000187 | |
| Spermine | Metabolite | hmdb:HMDB0001256 | |
| Tryptophan | Metabolite | hmdb:HMDB0000929 | |
| Oxobutyrate | Metabolite | hmdb:HMDB0000005 | |
| P-enolpyruvate | Metabolite | hmdb:HMDB0000263 | |
| Guanidinoacetate P | Metabolite | hmdb:HMDB0003705 | |
| Lactate | Metabolite | hmdb:HMDB0000190 | |
| OH-indoleacetate | Metabolite | hmdb:HMDB0000763 | |
| methylmalonyl-CoA | Metabolite | chebi:15465 | |
| Alanine | Metabolite | hmdb:HMDB0000161 | |
| Guanidinoacetate | Metabolite | hmdb:HMDB0000128 | |
| Succinate | Metabolite | hmdb:HMDB0000254 | |
| valine | Metabolite | hmdb:HMDB0000883 | |
| Phenylalanine | Metabolite | hmdb:HMDB0000159 | |
| oxo-methyl-valerate | Metabolite | chebi:35146 | |
| oxo-isovalerate | Metabolite | chebi:11851 | |
| Putrescine | Metabolite | hmdb:HMDB0001414 | |
| Pyruvate | Metabolite | hmdb:HMDB0000243 | |
| methylmalonate semialdehyde | Metabolite | chebi:16256 | |
| Serotonin | Metabolite | hmdb:HMDB0000259 | |
| Fumarate | Metabolite | hmdb:HMDB0000134 | |
| Dihydro-orotate | Metabolite | hmdb:HMDB0003349 | |
| Glutamate | Metabolite | hmdb:HMDB0000148 | |
| Malate | Metabolite | hmdb:HMDB0000156 | |
| Proline | Metabolite | hmdb:HMDB0000162 | |
| Indoleacetaldehyde | Metabolite | hmdb:HMDB0001190 | |
| Cysteine | Metabolite | hmdb:HMDB0000574 | |
| HCO3 | Metabolite | hmdb:HMDB0003538 | |
| NADP | Metabolite | hmdb:HMDB0000217 | |
| Met-tRNA | Metabolite | chebi:16635 | |
| Arginino-succinate | Metabolite | hmdb:HMDB0000052 | |
| N-Formylkynurenine | Metabolite | hmdb:HMDB0001200 | |
| Arg-tRNA | Metabolite | chebi:18366 | |
| Ala-tRNA | Metabolite | chebi:17732 | |
| Trp-tRNA | Metabolite | chebi:29159 | |
| isobutyryl-CoA | Metabolite | chebi:15479 | |
| Val-tRNA | Metabolite | chebi:29164 | |
| Leu-tRNA | Metabolite | chebi:16624 | |
| Ile-tRNA | Metabolite | chebi:29160 | |
| Isovaleryl-CoA | Metabolite | hmdb:HMDB0001113 | |
| Methylbutyryl-CoA | Metabolite | hmdb:HMDB0001041 | |
| Acetyl-CoA | Metabolite | hmdb:HMDB0001206 | |
| OH-methylglutaryl-CoA | Metabolite | hmdb:HMDB0001375 | |
| methacrylyl-CoA | Metabolite | chebi:27754 | |
| OH-isobutyrate | Metabolite | chebi:19641 | |
| Tiglyl-CoA | Metabolite | hmdb:HMDB0002054 | |
| OH-isovaleryl-CoA | Metabolite | hmdb:HMDB0006870 | |
| Methylacetoacetyl-CoA | Metabolite | hmdb:HMDB0001157 | |
| OH-isobutyryl-CoA | Metabolite | hmdb:HMDB0001052 | |
| Methylcrotonyl-CoA | Metabolite | hmdb:HMDB0001493 | |
| Methyl-OH-butyryl-CoA | Metabolite | hmdb:HMDB0001356 | |
| Propionyl-CoA | Metabolite | hmdb:HMDB0001275 | |
| Methylglutaconyl-CoA | Metabolite | hmdb:HMDB0001057 | |
| Acetyl-CoA | Metabolite | hmdb:HMDB0001206 | |
| His-tRNA | Metabolite | chebi:29155 | |
| pyrroline carboxylate | Metabolite | hmdb:HMDB0006875 | |
| Glu-tRNA | Metabolite | chebi:29157 | |
| glutamate semialdehyde | Metabolite | chebi:15757 | |
| glutamyl-P | Metabolite | chebi:21314 | |
| Imidazole acetaldehyde | Metabolite | hmdb:HMDB0003905 | |
| 2-oxo-glutarate | Metabolite | chebi:16810 | |
| glutamyl-cysteine | Metabolite | chebi:17515 | |
| Red. Glutathione | Metabolite | hmdb:HMDB0000125 | |
| R-S-glutathione | Metabolite | chebi:17021 | |
| Ox. glutathione | Metabolite | hmdb:HMDB0003337 | |
| Phe-tRNA | Metabolite | chebi:29153 | |
| homogentisate | Metabolite | chebi:16169 | |
| Epinephrine | Metabolite | hmdb:HMDB0000068 | |
| Norepinephrine | Metabolite | hmdb:HMDB0000216 | |
| Tyr-tRNA | Metabolite | chebi:29161 | |
| Gsr | GeneProduct | mgi:MGI:95804 | |
| Hdc | GeneProduct | mgi:MGI:96062 | |
| Cbs | GeneProduct | mgi:MGI:88285 | |
| Sms | GeneProduct | mgi:MGI:109490 | |
| Mdh1 | GeneProduct | mgi:MGI:97051 | |
| Gst | GeneProduct | mgi:MGI:1309515 | |
| Pkm2 | GeneProduct | mgi:MGI:97591 | |
| Ass1 | GeneProduct | mgi:MGI:88090 | |
| Aoc3 | GeneProduct | mgi:MGI:1306797 | |
| Eprs | GeneProduct | mgi:MGI:97838 | |
| Dld | GeneProduct | mgi:MGI:107450 | |
| Pck1 | GeneProduct | mgi:MGI:97501 | |
| Glud | GeneProduct | mgi:MGI:95753 | |
| Hmgcs2 | GeneProduct | mgi:MGI:101939 | |
| Hnmt | GeneProduct | mgi:MGI:2153181 | |
| Ddc | GeneProduct | mgi:MGI:94876 | |
| Acadm | GeneProduct | mgi:MGI:87867 | |
| Got2 | GeneProduct | mgi:MGI:95792 | |
| Auh | GeneProduct | mgi:MGI:1338011 | |
| Pdk4 | GeneProduct | mgi:MGI:1351481 | |
| Prodh | GeneProduct | ncbigene:19125 | |
| Dlst | GeneProduct | mgi:MGI:1926170 | |
| Fah | GeneProduct | mgi:MGI:95482 | |
| Ehhadh | GeneProduct | mgi:MGI:1277964 | |
| Hal | GeneProduct | mgi:MGI:96010 | |
| Iars | GeneProduct | mgi:MGI:2145219 | |
| Aldh1a1 | GeneProduct | mgi:MGI:1353450 | |
| Hibch | GeneProduct | mgi:MGI:1923792 | |
| Tat | GeneProduct | mgi:MGI:98487 | |
| Cad | GeneProduct | mgi:MGI:1916969 | |
| Mars2 | GeneProduct | mgi:MGI:2444136 | |
| Bhmt | GeneProduct | mgi:MGI:1339972 | |
| Bcat1 | GeneProduct | mgi:MGI:104861 | |
| Acaa1 | GeneProduct | mgi:MGI:2148491 | |
| Hibadh | GeneProduct | mgi:MGI:1889802 | |
| Gpt | GeneProduct | mgi:MGI:1915391 | |
| P4ha2 | GeneProduct | mgi:MGI:894286 | |
| Pdha1 | GeneProduct | ncbigene:18597 | |
| Tpo | GeneProduct | mgi:MGI:98813 | |
| Gclc | GeneProduct | mgi:MGI:104995 | |
| Acadm | GeneProduct | mgi:MGI:87867 | |
| Adh5 | GeneProduct | mgi:MGI:87929 | |
| Oat | GeneProduct | mgi:MGI:97394 | |
| pdhp | GeneProduct | ncbigene:242083 | |
| Acadm | GeneProduct | mgi:MGI:87867 | |
| Adh4 | GeneProduct | mgi:MGI:1349472 | |
| Ddc | GeneProduct | mgi:MGI:94876 | |
| Bcat1 | GeneProduct | mgi:MGI:104861 | |
| Maoa | GeneProduct | mgi:MGI:96915 | |
| Th | GeneProduct | mgi:MGI:98735 | |
| Sds | GeneProduct | mgi:MGI:98270 | |
| Cad | GeneProduct | mgi:MGI:1916969 | |
| Lars2 | GeneProduct | mgi:MGI:2142973 | |
| G6Pase | GeneProduct | ncbigene:14378 | |
| Wars | GeneProduct | mgi:MGI:104630 | |
| Ldh1 | GeneProduct | mgi:MGI:96759 | |
| Adh1 | GeneProduct | mgi:MGI:87921 | |
| Gls | GeneProduct | mgi:MGI:95752 | |
| Sdha | GeneProduct | mgi:MGI:1914195 | |
| phtRNAs | GeneProduct | mgi:MGI:1346035 | |
| Asns | GeneProduct | mgi:MGI:1350929 | |
| Pdha1 ina | GeneProduct | ncbigene:18597 | |
| Aldh7a1 | GeneProduct | mgi:MGI:108186 | |
| Mpst | GeneProduct | mgi:MGI:2179733 | |
| Suclg1 | GeneProduct | mgi:MGI:1927234 | |
| Hmgcl | GeneProduct | mgi:MGI:96158 | |
| Adh7 | GeneProduct | mgi:MGI:87926 | |
| Ddc | GeneProduct | mgi:MGI:94876 | |
| Pcx | GeneProduct | mgi:MGI:97520 | |
| Ehhadh | GeneProduct | mgi:MGI:1277964 | |
| Pycr1 | GeneProduct | mgi:MGI:2384795 | |
| Gpt | GeneProduct | mgi:MGI:1915391 | |
| Ogdh | GeneProduct | ncbigene:18293 | |
| Tat | GeneProduct | mgi:MGI:98487 | |
| Aldh7a1 | GeneProduct | mgi:MGI:108186 | |
| Asl | GeneProduct | mgi:MGI:88084 | |
| Gss | GeneProduct | mgi:MGI:95852 | |
| Fh1 | GeneProduct | ncbigene:14194 | |
| Cth | GeneProduct | mgi:MGI:1339968 | |
| Tph1 | GeneProduct | mgi:MGI:98796 | |
| Mut | GeneProduct | mgi:MGI:97239 | |
| Arg1 | GeneProduct | mgi:MGI:88070 | |
| Maoa | GeneProduct | mgi:MGI:96915 | |
| Mdh2 | GeneProduct | mgi:MGI:97050 | |
| Idh1 | GeneProduct | mgi:MGI:96413 | |
| Pnmt | GeneProduct | mgi:MGI:97724 | |
| Dbh | GeneProduct | mgi:MGI:94864 | |
| Aco2 | GeneProduct | mgi:MGI:87880 | |
| Glns | GeneProduct | mgi:MGI:95739 | |
| Sds | GeneProduct | mgi:MGI:98270 | |
| Rars | GeneProduct | mgi:MGI:1914297 | |
| Mccc1 | GeneProduct | mgi:MGI:1919289 | |
| Odc | GeneProduct | mgi:MGI:97402 | |
| Gftcd | GeneProduct | mgi:MGI:1339962 | |
| Pycs | GeneProduct | mgi:MGI:1888908 | |
| Got1 | GeneProduct | mgi:MGI:95791 | |
| Cs | GeneProduct | mgi:MGI:88529 | |
| Acly | GeneProduct | mgi:MGI:103251 | |
| Vars2 | GeneProduct | mgi:MGI:90675 | |
| Pdhx | GeneProduct | mgi:MGI:1351627 | |
| Tdo2 | GeneProduct | mgi:MGI:1928486 | |
| Otc | GeneProduct | mgi:MGI:97448 | |
| Sdhd | GeneProduct | mgi:MGI:1914175 | |
| Acas2l | GeneProduct | mgi:MGI:1915988 | |
| CPS | GeneProduct | mgi:MGI:891996 | |
| Maoa | GeneProduct | mgi:MGI:96915 | |
| Srm | GeneProduct | mgi:MGI:102690 | |
| Hadhsc | GeneProduct | mgi:MGI:96009 | |
| Pycs | GeneProduct | mgi:MGI:1888908 | |
| Bcat1 | GeneProduct | mgi:MGI:104861 | |
| Ehhadh | GeneProduct | mgi:MGI:1277964 | |
| Arg2 | GeneProduct | mgi:MGI:1330806 |